Giant sacrococcygeal teratoma in newborns Yenidoğanda dev sakrokoksigeal teratom
نویسندگان
چکیده
Fig. 2 A sacrococcygeal teratoma is a tumor that develops at the base of the coccyx. It occurs in 1 out of every 35,000–40,000 live births and is the most common tumor in newborns [1]. The tumor originates during embryonic development when the primitive streak fails to differentiate among mesodermal, ectodermal, and endodermal tissues in the embryonic disc [2]. A 2850 g girl was born by cesarean delivery to a healthy 32-year-old mother after an uncomplicated gestation of 38 weeks. At birth, the healthy, actively crying infant was found to have a large mass attached to her sacrococcygeal region. A magnetic resonance imaging (MRI) scan showed a regularly marginated, thinwalled 6 x 12 x 15 cm cystic presacral tumor that was exerting significant mass effect and displacing the patient’s rectum, anus and gluteal muscles. The MRI showed two distinct, well-circumscribed, thin-walled cystic components with homogeneous high protein and serous fluid contents. The solid portion of the mass contained large fatty tissue that had a high signal on T1and T2-weighted MR images and decreased signal intensity on T2-weighted images with fat suppression (Figures 1, 2). The patient was referred to our pediatric department to be assessed for surgical correction. Surgery was performed when the baby was 1 week old, and the mass was excised. Histopathological examination of the excised mass confirmed sacrococcygeal teratoma.
منابع مشابه
A case of a giant sacrococcygeal teratoma.
Sacrococygeal teratomas are congenital tumors of newborns, originate from one or more of the three germinal layers. Most sacrococygeal teratomas are found in newborns, infants and children youger than 4 years. The prenatal ultrasound exams have increased the number of sacrococygeal teratomas presenting in fetuses. Radical resection, including the coccyx must be performed even if the primary les...
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